Korean Circ J.  2003 Oct;33(10):928-932. 10.4070/kcj.2003.33.10.928.

Left Pulmonary Artery Agenesis Accompanied with Fistula of Left Circumplex Artery to Left Bronchial Artery

• Park DY
• Lee NH
• Choi SH
• Yun IS
• Park KH
• Jung CS
• Ko JS
• Nam DI
• Kim DS
• Choi CH
• Han KW

• KMID: 1938808
• DOI: http://doi.org/10.4070/kcj.2003.33.10.928

Abstract

Left pulmonary artery agenesis, accompanied by a coronary arterial fistula, is a very rare anomaly. Although unilateral pulmonary artery agenesis is associated with other cardiovascular defects, like as ventricular septal defect, patent ductus arteriosus, and tetralogy of fallot, this anomaly, accompanied by a coronary arterial fistula, has not yet been reported. Most patients with no associated cardiac anomalies have only minor, or absent, symptoms, and survive to adulthood, but some patients may suffer from recurrent respiratory infections and hemoptysis. The vessel to the affected lung in many of the proved cases has been described as arising from either the bronchial artery or the aortic arch. The blood supply from the coronary artery to the affected lung has never been reported. Recently, a case of left pulmonary artery agenesis, accompanied with a coronary arterial fistula was experienced, which was diagnosed by coronary angiography and a chest CT, which is presented, with the review of relevant literature.

Keyword

Pulmonary artery agenesis; Coronary arterial fistula

MeSH Terms

Aorta, Thoracic
Arteries*
Bronchial Arteries*
Coronary Angiography
Coronary Vessels
Ductus Arteriosus, Patent
Fistula*
Heart Septal Defects, Ventricular
Hemoptysis
Humans
Lung
Pulmonary Artery*
Respiratory Tract Infections
Tetralogy of Fallot
Tomography, X-Ray Computed