Korean J Anesthesiol.  2005 Oct;49(4):563-566. 10.4097/kjae.2005.49.4.563.

Anesthesia for Living Related Liver Transplantation in Argininosuccinic Acidemia: A case report

Affiliations
  • 1Department of Anesthesiology and Pain Medicine, Yonsei University College of Medicine, Seoul, Korea. nsh66@yumc.yonsei.ac.kr
  • 2Anesthesia and Pain Research Institute, Yonsei University College of Medicine, Seoul, Korea.

Abstract

We describe our initial experience of the perioperative anesthetic care provided to 8 years old female child with argininosuccinic acidemia undergoing living-related liver transplantation because it is the only available therapy for end-stage liver disease. Induction and maintenance of anesthesia has been conventional method. Arterial catheterized at radial and femoral arteries for continuous blood pressure monitoring and sampling. 18 G central vein catheterization was placed in left subclavian vein for fluid, drug infusion and CVP monitoring. EKG, pulse oxymetry, end-tidal CO2, urine output and body temperature were monitored. CBC, PT, aPTT, serum electrolyte were checked at preanhepatic, anhepatic phase and just after hepatic artery anastomosis. ABGA was checked every 1 hour. The level of serum ammmonia returned to normal range without protein restriction. We describe this case and a brief review of the literature.

Keyword

argininosuccinic acidemia; liver transplantation

MeSH Terms

Anesthesia*
Argininosuccinic Aciduria*
Blood Pressure Monitors
Body Temperature
Catheterization
Catheters
Child
Electrocardiography
Female
Femoral Artery
Hepatic Artery
Humans
Liver Diseases
Liver Transplantation*
Liver*
Reference Values
Subclavian Vein
Veins
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