Korean J Dermatol.  1999 Oct;37(10):1535-1537.

A Case of Malignant Peripheral Nerve Sheath Tumor in Neurofibromatosis

Affiliations
  • 1Department of Dermatology, College of Medicine, The Catholic University of Korea, Seoul, Korea.
  • 2Department of Surgery, College of Medicine, The Catholic University of Korea, Seoul, Korea.

Abstract

Malignant peripheral nerve sheath tumor is a neoplasm that most often arises in anatomically discernible peripheral nerves or neurofibroma. A 37-year-old woman presented with a rapid growing pedunculated, huge mass on the left breast for 1 month. She has suffered from neurofibromatosis type 1 with multiple cafe au lait spots and neurofibromas. The huge mass has developed from a subcutaneous nodule on the left breast. The clinical and histopathological data showed a malignant peripheral nerve sheath tumor. Since no sign of the metastasis was observed, local excision was performed. We, herein, report a case of malignant peripheral nerve sheath tumor developed in the patient of nurofibromatosis type 1.

Keyword

Malignant peripheral nerve sheath tumor; Neurofibromatosis

MeSH Terms

Adult
Breast
Cafe-au-Lait Spots
Female
Humans
Neoplasm Metastasis
Neurofibroma
Neurofibromatoses*
Neurofibromatosis 1
Peripheral Nerves*
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