Korean J Thorac Cardiovasc Surg.  2007 Nov;40(11):793-797.

A Communicating Bronchopulmonary Foregut Malformation Associated with Absence of the Left Pericardium: A case report

• Yoo DG
• Kim CW
• Park CB
• Kang PJ
• Lee JH

Abstract

A communicating bronchopulmonary foregut malformation (CBPFM) is a rare congenital anomaly that is characterized by a fistula between isolated respiratory tissue and the esophagus or stomach. The presence of accessory lung tissue arising from the primitive gastrointestinal tube is a common factor in the development of all forms of bronchopulmonary foregut malformations. Recurrent pneumonia associated with cystic radiographic structures is a characteristic of the condition. Further imaging studies using esophagogram, bronchography, computerized tomography, MRI, and arteriography can help in making a diagnostic evaluation. The treatment is a surgical resection of the involved lung tissue, and fistula closure with a good prognosis. We encountered a case of CBPFM, who presented with an extralobar pulmonary sequestration and bronchogenic cyst communicating with a tubular esophageal duplication that was associated with a complete left pericardial defect.

Keyword

Esophageal congenital anomalies; Lung anomaly; Pericardium

MeSH Terms

Angiography
Bronchogenic Cyst
Bronchography
Bronchopulmonary Sequestration
Esophagus
Fistula
Lung
Magnetic Resonance Imaging
Pericardium*
Pneumonia
Prognosis
Stomach