J Korean Surg Soc.  2004 Apr;66(4):354-357.

Mucin-Producing Intrahepatic Cholangiocelluar Carcinoma Presenting as a Focal Dilatation of the Intrahepatic Bile Duct

• Kim JD
• Jang HJ
• Cho YP
• Kim YH
• Jung SM
• Kang KH
• Han MS

Abstract

A case of a mucin-producing intrahepatic cholangiocellular carcinoma (MPCC) is reported. A 58-year old female presented with epigastric discomfort of several years duration. The physical examination and laboratory findings were normal. Abdominal ultrasonography (US) and computed tomography (CT) showed a focal dilatation of the right posterior intrahepatic bile duct. There was no abnormal mass in the liver parenchyma. Endoscopic retrograde cholangiopancreaticography (ERCP) showed a filling defect in the right posterior hepatic duct. There was no anatomical abnormality and abnormal staining on the heaptic angiography. At the operation, the right posterior hepatic duct was filled with mucin. The patient had a right posterior segmentectomy. Histologically, a 2.5 X 0.6 X 0.6 cm sized mucin-producing intrahepatic cholangiocellular carcinoma was found in segment 6 of the liver. The postoperative recovery was good, and the patient has had a good social life for the last 3 years, with no evidence of tumor recurrence. In patients with a focal dilatation of the intrahepatic bile duct on CT or US with no underlying cause, an intrahepatic malignancy has to be suspected.

Keyword

Mucin-producing intrahepatic cholangiocellular carcinoma (MPCC); Focal dilatation of intrahepatic bile duct

MeSH Terms

Angiography
Bile Ducts, Intrahepatic*
Cholangiocarcinoma
Dilatation*
Female
Hepatic Duct, Common
Humans
Liver
Mastectomy, Segmental
Middle Aged
Mucins
Physical Examination
Recurrence
Ultrasonography
Mucins