Korean J Dermatol.  2006 Oct;44(10):1228-1230.

A Case of Pseudoxanthoma-elasticum-like Papillary Dermal Elastolysis

• Goo B
• Lee JH
• Lee KH

Abstract

Pseudoxanthoma elasticum-like papillary dermal elastolysis is a disorder of the dermis, characterized by clinical features similar to pseudoxanthoma elasticum and the pathologic features of elastolysis limited to the papillary dermis, such as sun-protected, intrinsically-aged skin. A 64-year old woman presented with a 7 year history of a localized skin lesion on the back of her neck. Physical examination revealed skin to yellow colored, non-follicular grouped uniform papules, sized 5~8 mm, and coalescent plaques localized below the hair line. Histopathologic and immunohistochemical findings of decrease and elastolysis of the elastic fibers in the papillary dermis confirmed the diagnosis. In this article, we report a case of pseudoxanthoma elasticum-like papillary dermal elastolysis which presented with typical clinical and pathologic features.

Keyword

Intrinsic skin aging; Pseudoxanthoma elasticum-like papillary dermal elastolysis

MeSH Terms

Dermis
Diagnosis
Elastic Tissue
Female
Hair
Humans
Middle Aged
Neck
Physical Examination
Pseudoxanthoma Elasticum
Skin