Korean J Med.  2001 Apr;60(4):388-392.

A case of Von Meyenburg Complex associated with calculous cholecystitis, cerebral aneurysm and renal cortical cyst

Affiliations
  • 1Department of Internal medicine, Myung-Ji St.mary's Hospital, Seoul, Korea.
  • 2Department of General surgery, Myung-Ji St.mary's Hospital, Seoul, Korea.
  • 3Department of Neurosurgery, Myung-Ji St.mary's Hospital, Seoul, Korea.
  • 4Department of Radiology, Myung-Ji St.mary's Hospital, Seoul, Korea.
  • 5Department of Pathology, Myung-Ji St.mary's Hospital, Seoul, Korea. haeng1@kornet.net

Abstract

Von Meyenburg complexes (VMC) have many synonyms such as bile duct hamartomas and biliary hamartoma. These rare benign disorders are considered as congenital diseases caused by malformed differentiation of ductal plate. The diagnosis of VMC by common radiologic modality such as ultrasound and computed tomography was nearly impossible until the emergence of cholangiopancreatography by magnetic resonance imaging (MRCP) and the pathologic examination was the only way to confirm the diagnosis of VMC. But MRCP is now considered as most accurate noninvasive method for diagnosis of VMC. We report a histologically proven case of VMC associated with calculous cholecystitis, cerebral aneurysm and renal cortical cyst. To our knowledge, no comparable case has been reported and this would be the only second reported case of VMC, which was diagnosed by MRCP.

Keyword

Von meyenburg complex; Bile duct hamartoma; MRCP

MeSH Terms

Bile Ducts
Cholecystitis*
Diagnosis
Hamartoma
Intracranial Aneurysm*
Magnetic Resonance Imaging
Ultrasonography
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