Korean J Nephrol.  2010 May;29(3):376-380.

Idiopathic Retroperitoneal Fibrosis Associated with a Horseshoe Kidney

Affiliations
  • 1Division of Nephrology, Department of Internal Medicine, Chonnam National University Medical School, Gwangju, Korea. nhk111@chonnam.ac.kr
  • 2Department of Urology, Chonnam National University Medical School, Gwangju, Korea.
  • 3Department of Radiology, Chonnam National University Medical School, Gwangju, Korea.

Abstract

A case of a 52-year-old man with retroperitoneal fibrosis and a horseshoe kidney is presented. Horseshoe kidney is one of the most common renal anomalies and complicated with urinary tract infection, hydronephrosis, calculi, tumor of the renal pelvis, and other multiple congenital abnormalities. Idiopathic retroperitoneal fibrosis is a rare disease characterized by the presence of a retroperitoneal tissue, consisting of chronic inflammation and marked fibrosis, which often entraps ureters or other abdominal organs. The correlation between horseshoe kidney and retroperitoneal fibrosis has not been described. We report a rare case of idiopathic retroperitoneal fibrosis with horseshoe kidney disease demonstrating good response to steroid therapy.

Keyword

Hydronephrosis; Retroperitoneal fibrosis; Steroids

MeSH Terms

Calculi
Congenital Abnormalities
Fibrosis
Humans
Hydronephrosis
Inflammation
Kidney
Kidney Diseases
Kidney Pelvis
Middle Aged
Rare Diseases
Retroperitoneal Fibrosis
Steroids
Ureter
Urinary Tract Infections
Steroids
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