Korean Circ J.  2011 Aug;41(8):494-496. 10.4070/kcj.2011.41.8.494.

Modified Damus-Kaye-Stansel/Dor Procedure for a Newborn With Severe Left Ventricular Aneurysm

• Seo DM
• Won HS
• Ko JK
• Jhang WK

• KMID: 1826361
• DOI: http://doi.org/10.4070/kcj.2011.41.8.494

Abstract

Congenital left ventricular aneurysm (CVA) is a rare cardiac malformation. The prognosis is variable, depending on such factors as the size in comparison to the ventricular cavity, signs of heart failure, arrhythmia and so on. Most infants and young children with large aneurysm showed poor clinical outcomes. Here, we report the case of patient who was prenatally diagnosed with a large CVA, who had severe left ventricular dysfunction at 21 weeks' gestation for which she successfully underwent a modified Damus-Kaye-Stansel/Dor procedure.

Keyword

Heart aneurysm; Surgical procedures, operative

MeSH Terms

Aneurysm
Arrhythmias, Cardiac
Child
Heart Aneurysm
Heart Failure
Humans
Infant
Infant, Newborn
Pregnancy
Prognosis
Surgical Procedures, Operative
Ventricular Dysfunction, Left

Figure

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  Fig. 1 Fetal echocardiographs at 21+6 weeks gestation, showing an apical left ventricular aneurysm which became aggravated during follow-up.

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  Fig. 2 Postnatal echocardiography, showing a markedly enlarged LV aneurysm that was too large to permit proper LV function. LV: left ventricular.

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  Fig. 3 Postoperative echocardiography, showing a restored LV geometry and decreased LV dimension after LV aneurysmal tissue resection with endoventricular reductoplasty, using a Dacron patch. LV: left ventricular.

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