J Clin Neurol.  2007 Dec;3(4):204-207. 10.3988/jcn.2007.3.4.204.

Idiopathic Spinal Cord Herniation as a Treatable Cause of Progressive Brown-Sequard Syndrome

• Kim JM
• Oh SH
• Kim KJ
• Park SH
• Park KS

• KMID: 1808559
• DOI: http://doi.org/10.3988/jcn.2007.3.4.204

Abstract

Idiopathic spinal cord herniation is a rare spinal cord disorder caused by spinal cord prolapse through a adural defect. It is a curable disease, so early detection is of particular importance. We report a 38-year-old woman with Brown-Sequard syndrome which was caused by the thoracic spinal cord herniation. Her weakness was almost completely resolved after surgical management, which emphasizes the importance of early diagnosis and surgical management in this rare disease entity.

Keyword

Idiopathic spinal cord herniation; Brown-Sequard syndrome; Treatment; Surgery

MeSH Terms

Adult
Brown-Sequard Syndrome*
Early Diagnosis
Female
Humans
Prolapse
Rare Diseases
Spinal Cord Diseases
Spinal Cord*

Figure

• 

  Figure 1 Initial cervicothoracic spine MRI showing anterior displacement of spinal cord at the level of the T4-5 disc (arrows).

• 

  Figure 2 Spine MRI performed 3 days after surgery showing restored spinal cord contour at the level of the T4-5 disc (arrow).

Reference

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