Korean J Anesthesiol.  2008 Apr;54(4):459-463. 10.4097/kjae.2008.54.4.459.

Relapsing Polychondritis with Subglottic Stenosis Diagnosed after Tonsillectomy: A case report

• Sung CH
• Park JH
• Lim SJ
• Choi YW

• KMID: 1763291
• DOI: http://doi.org/10.4097/kjae.2008.54.4.459

Abstract

Relapsing polychondritis (RP) is a rare autoimmune connective tissue disease of unclear pathogenesis and may present with the multisystem involvements and varied presentations, courses and responses to the therapy. The respiratory complaints or history such as dyspnea or snoring deserve to be in consideration, especially in the cases of no specific causes and must be ruled out the rare autoimmune airway diseases such as relapsing polychondritis, Wegener's granulomatosis, rhinoscleroma, or amyloidosis resulting in serious airway obstruction without adequate management. In this report we described a case of 15-year-old young male with the delayed diagnosis of relapsing polychondritis with intractable subglottic stenosis during the course of the management for several months despite of tonsillectomy for the relief of the airway obstruction.

Keyword

airway obstruction; subglottic stenosis; tonsillectomy

MeSH Terms

Adolescent
Airway Obstruction
Amyloidosis
Connective Tissue Diseases
Constriction, Pathologic
Delayed Diagnosis
Dyspnea
Humans
Male
Polychondritis, Relapsing
Rhinoscleroma
Snoring
Tonsillectomy
Wegener Granulomatosis