J Korean Soc Radiol.  2014 Sep;71(3):132-135. 10.3348/jksr.2014.71.3.132.

Primary Renal Osteosarcoma Presenting as Hydronephrotic Kidney: A Case Report with Imaging Findings and a Literature Review

• Lee JW
• Koo JH
• Kim YM

• KMID: 1736478
• DOI: http://doi.org/10.3348/jksr.2014.71.3.132

Abstract

Primary renal osteosarcoma is an extraordinarily rare primary tumor of the kidney. It occurs mostly in middle-aged and older individuals, and generally presents with non-specific symptoms such as abdominal pain, weight loss, palpable mass, and gross hematuria. Radiographically bizarre renal calcifications are often indicative of this uncommon neoplasm. Herein we report a case of primary osteosarcoma in a hydronephrotic kidney of a 76-year-old man, who developed lung metastasis soon after a radical nephrectomy. To the best of our knowledge, this is the first computed tomography based report of a patient with the hydronephrotic form of primary renal osteosarcoma.

MeSH Terms

Abdominal Pain
Aged
Hematuria
Humans
Kidney*
Lung
Multidetector Computed Tomography
Neoplasm Metastasis
Nephrectomy
Osteosarcoma*
Weight Loss

Figure

• 

  Fig. 1 A 76-year-old man with primary renal osteosarcoma. A. Simple radiography shows soft tissue density mass on the left side of abdomen with calcifications (arrows). B, C. Precontrast CT scans show amorphous or nodular calcifications and irregular soft tissue components (arrows) within the mass. D. Postcontrast axial CT scan shows irregular enhancing solid areas along the peripheral and central portion of the mass with focal fat obliteration between the mass and left descending colon (arrows). E. Postcontrast coronal reformatted CT scan shows irregular enhancing solid areas with calcifications in the lower portion of marked hydronephrotic left kidney (arrows). F. Photomicrograph of specimen shows immature neoplastic osteoids and sarcomatous stroma (H&E, × 100).

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