Korean J Pathol.
1986 Jun;20(2):199-202.
Congenital Absence of Intestinal Musculature Associated with Long Segment Hirschsprung's Disease
- Affiliations
-
- 1Department of Pathology, School of Medicine, Han Yang University, Seoul, Korea.
- 2Department of General Surgery, School of Medicine, Han Yang University, Seoul, Korea.
Abstract
- Intestinal obstruction is the commonest cause for emergency surgical intervention in the newborn. An extremely rare cause of intestinal obstruction in the neonate is a congenital abnormality consisting of segmental absence of intestinal musculature with intact serosa and mucosa. This report represents not only the fourth reported case of this anomaly but also the first case associated with long segment Hirschsprung's disease in English-written literatures.
