Korean J Radiol.  2014 Feb;15(1):61-65. 10.3348/kjr.2014.15.1.61.

Malignant Glomus Tumor of the Peritoneum: Case Report

• Baleato-Gonzalez S
• Garcia-Figueiras R
• Trujillo-Ariza MV
• Carrera-Alvarez JJ

• KMID: 1711478
• DOI: http://doi.org/10.3348/kjr.2014.15.1.61

Abstract

Glomus tumors are usually benign tumors that occur in the skin and soft tissues of the extremities. Visceral locations, such as stomach, intestines or lung, are extremely rare because glomus bodies are rare or absent in these organs. This report describes our experience in a 47-year-old woman diagnosed with a peritoneal malignant glomus tumor. This finding has not been previously reported.

Keyword

Peritoneal tumors; Malignant glomus tumor; Glomangiosarcoma

MeSH Terms

Female
Glomus Tumor/pathology/*radiography
Humans
Middle Aged
Peritoneal Neoplasms/pathology/*radiography
Sarcoma
Tomography, X-Ray Computed

Figure

• 

  Fig. 1 CT and staining observations.A. Axial CT after contrast administration in portal phase shows large mass that involved peritoneal surface without visceral organ affected. B. Coronal reformatted CT after contrast administration in portal phase demonstrates inframesocolic and paracolic gutters mass with heterogeneous enhancement and few small foci inside (arrows). C. Hematoxylin and eosin stain (20 x) shows glomus body consisting of uniform small, rounded cells with centrally placed round and pleomorphic nuclei. These cells are located around vessels. D. Smooth muscle actin immunostain demonstrating strong cytoplasmic positivity.

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