Korean J Dermatol.  1989 Aug;27(4):474-476.

A Case of Childhood Dermatofibrosarcoma Protuberans

Abstract

Dermatofibrosarcoma protuberans(DFSP) is a rare, distinctive cutsneous tumor originating in the dermis that appears as a raised uninodular or multinodular lesion on the trunk or the proximal extremities. In about 10% of the cases, DFSP arises in childhood and it is rarely evident already at birth. Histopathologically, DFSP shows the chsracteristic storiform and cartwheel patterns, with the fibroblasts arranged radially about a small central hub of fibrous tissue. We report herein a case of childhood DFSP in a 7-year-old boy.

Keyword

Childhood; Dermatofibrosarcoma protuberans

MeSH Terms

Child
Dermatofibrosarcoma*
Dermis
Extremities
Fibroblasts
Humans
Male
Parturition
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