Korean J Dermatol.  1978 Jun;16(3):261-271.

Two Cases of Xeroderma Pigmentosum

• Suh MS
• Hahm JH
• Kook HI

Abstract

Xeroderma pigmentosum is a hereditary disorder characterized by the early development of pigmentary chnges, atropht, keratoses, and carcinoma, predominantly light exposed area skin.Two cases of xeroderma pigmentosum complicated by basal cell Ca. were presented. The one was 15 years old male who had been suffered from pea to walnut sized multiple tumors and ulcers on the face with scattered brownish macuIes on the eun exposed area since about 9 years old of his age. The other was 22 years old maIe who had been suffered from the same skin lesions as the former on the face, neck and dorsum of hands. In both cases skin lesions aggravated during each summer seasons and there were on history of convulsions and other neurological symptoms Histopathological findings of tumors on both cases revealed typical findings of basal cell Ca.

MeSH Terms

Adolescent
Child
Hand
Humans
Ichthyosis*
Juglans
Keratosis
Male
Neck
Peas
Seasons
Seizures
Skin
Ulcer
Xeroderma Pigmentosum*
Young Adult