Korean J Pediatr.
2004 Apr;47(4):462-464.
Surgical Correction of Congenital Heart Disease In 18 Trisomy
- Affiliations
-
- 1Department of Pediatrics, Sejong General Hospital, Buncheon, Korea. amyjys@hanmail.net
- 2Department of Pediatrics, College of Medicine, Kyunghee University, Seoul, Korea.
- 3Department of Thoracic Surgery, Seoul National University College of Medicine, Seoul, Korea.
Abstract
- 18 trisomy(Edwards syndrome) is a fatal disease with a congenital heart anomaly. Patients usually receive less aggressive care because caregivers expect them to die very young. Although they have a very poor prognosis due to severe multi-organ dysfunction, symptomatic simple cardiac anomaly with left to right shunt can be repaired. We experienced a case of 18 trisomy with ventricular septal defect and patent ductus arteriosus. He showed prolonged dyspnea and tachypnea after the ligation of patent ductus arteriosus in a previous hospital. In our hospital, the ventricular septal defect was closed because his parents insisted on aggressive treatment. After surgery, the symptoms were relieved and he was discharged in a condition satisfactory to his parents and the medical team.