J Korean Pediatr Soc.
2001 Jan;44(1):89-93.
A Case of Distal Renal Tubular Acidosis Associated with Medullary Sponge Kidney
- Affiliations
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- 1Department of Pediatrics, School of Medicine, Keimyung University, Daegu, Korea.
- 2Department of Diagnostic Radiology, School of Medicine, Keimyung University, Daegu, Korea.
Abstract
- Renal tubular acidosis is a clinical state of systemic hyperchloremic acidosis resulting from impaired urine acidification. Medullary sponge kidney is a renal parenchymal malformation characterized by cystic dilatation of the collecting ducts. Although medullary sponge kidney is a congenital disease, it is rarely identified in childhood and is usually discovered in adulthood. Medullary sponge kidney patients may have defects in urinary acidification and concentration mechanism. We experienced a case of distal renal tubular acidosis associated with medullary sponge kidney. So, we report a case of distal renal tubular acidosis associated with medullary sponge kidney with a brief review of the related literature.
