J Korean Pediatr Soc.  1998 Jul;41(7):984-988.

A Case of Superior Mesenteric Artery Aneurysm associated with Marfan Syndrome

• Sung IH
• Kim SH
• Song MS
• Kim CH

Abstract

Superior mesenteric artery aneurysm is very rare complication of Marfan syndrome, especially in children. A 11 years old male patient was admitted to the hospital because of fluctuating high fever and diagnosed as infective endocarditis and Marfan syndrome. During antibiotics therapy, fever was slowly decreased but abdominal pain was developed and pulsatile abdominal mass was palpable in the midline of the abdomen. And the diagnosis was made as superior mesenteric artery aneurysm by ultrasonogaphy and abdominal aortogram. Resection of aneurysm was performed successfully. A brief review of the related literatures was made.

Keyword

Marfan syndrome; Infective endocarditis; Superior mesenteric artery aneurysm

MeSH Terms

Abdomen
Abdominal Pain
Aneurysm*
Anti-Bacterial Agents
Child
Diagnosis
Endocarditis
Fever
Humans
Hyperthermia, Induced
Male
Marfan Syndrome*
Mesenteric Artery, Superior*
Anti-Bacterial Agents