J Korean Soc Echocardiogr.
2003 Dec;11(2):108-113.
Two Cases of Spongy Myocardium Detected in Adult
- Affiliations
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- 1Department of Internal Medicine Daelim Saint Mary's Hospital, Seoul, Korea.
- 2Department of Internal Medicine, College of Medicine, The Catholic University of Korea, Seoul, Korea. younhj@catholic.ac.kr
Abstract
- Isolated noncompaction of the left ventricular myocardium is a rare cardiac disorder due to an arrest in myocardial morphogenesis. It is characterized by prominent and excessive trabeculation in a ventricular wall segment, with deep intertrabecular spaces perfused from the ventricular cavity. Echocardiographic findings are important clues for the diagnosis. Clinical symptoms include signs of left ventricular systolic dysfunction even to the point of heart failure, ventricular arrhythmias, and embolic events. We describe two cases of isolated noncompaction of the myocardium, with ventricular tachycardia in one, and chest pain due to microvascular dysfunction in the other.