J Korean Geriatr Soc.
2008 Jun;12(2):107-111.
Atypical Form of Motor Neuron Disease: Brachial Amyotrophic Diplegia
- Affiliations
-
- 1Department of Rehabilitation Medicine, Asan Medical Center, University of Ulsan College of Medicine, Seoul, Korea. kysmart@amc.seoul.kr
Abstract
- Brachial amyotrophic diplegia is a rare disease presenting with severe weakness that is completely confined to the upper limbs over time without upper motor neuron sign. It might be a stable and relatively benign variant of motor neuron disease and should be differentiated from other motor neuropathies. A 60-year-old man presented with a two year history of symmetrical muscle wasting and weakness in his arm and shoulder girdle. Bulbar and leg muscle were not affected and he was independent in ambulation. Nerve conduction studies revealed normal except the low amplitude of median and ulnar compound muscle action potential with no evidence of conduction block. Needle electromyography showed denervation potential and neuropathic motor unit action potential throughout the upper limb. We report this case with a brief review of related literatures.
- Full Text Links
-
- Actions
-
Cited
- CITED
-
- Close
- Share
-
- Similar articles
-
- Clinical Features of Brachial Amyotrophic Diplegia
- Clinical Characteristics, Electrodiagnostic, and Imaging Findings of Atypical Forms of Motor Neuron Disease
- Comparison between Flail Arm Syndrome and Upper Limb Onset Amyotrophic Lateral Sclerosis: Clinical Features and Electromyographic Findings
- Update of Therapeutic Clinical Trials for Amyotrophic Lateral Sclerosis
- A Case of Motor Neuron Disease Presenting as Dyspnea in the Emergency Department
