J Korean Soc Neonatol.
2008 Nov;15(2):176-182.
A Case of Congenital Intrahepatic Portosystemic Shunt Associated with VSD Detected by Antenatal Sonography and Treated with Four Coil Embolizations and Open Heart Surgery after Birth
- Affiliations
-
- 1Department of Pediatrics, Seoul National University College of Medicine, Seoul, Korea. neona@plaza.ac.kr
- 2Department of Radiology, Seoul National University College of Medicine, Seoul, Korea.
Abstract
- A congenital portosystemic shunt is a very rare portosystemic vascular anomaly which leads to jaundice, hypoglycemia, hyperammonemia, liver cirrhosis, hepatic coma, and pulmonary hypertension. Anatomically, portosystemic shunts are divided into intra- and extra- hepatic shunts. Congenital intrahepatic portosystemic shunts are rare anomalies, and the early diagnosis is important to prevent hepatic encephalopathy and hypoglycemia. We report a case of an infant with symptoms of heart failure due to a congenital intrahepatic portosystemic shunt and a ventricular septal defect (VSD), which were treated successfully with four coil embolizations and open heart surgery for the VSD.
Keyword
- Full Text Links
-
- Actions
-
Cited
- CITED
-
- Close
- Share
-
- Similar articles
-
- Congenital Intrahepatic Portosystemic Shunt in a Newbom Successfully Treated with Coil Embolization Via Umbilical Vein
- A Clinical Study of Congenital Intrahepatic Portosystemic Shunt Diagnosed in Neonatal Period
- A Case of Congenital Intrahepatic Portosystemic Venous Shunt
- Treating Sudden Onset Hepatic Encephalopathy with Coil Embolization in a Patient with a Congenital Intrahepatic Portosystemic Venous Shunt: A Case Report
- Intrahepatic Portosystemic Venous Shunt Presenting as a Cystic Mass in a Patient without Liver Cirrhosis: A Case Report
