Korean J Thorac Cardiovasc Surg.
2009 Dec;42(6):770-773.
Tetralogy of Fallot Associated with Multiple Cardiac Rhabdomyomas: case report
- Affiliations
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- 1Division of Pediatric Cardiac Surgery, Asan Medical Center, University of Ulsan College of Medicine, Korea. tjyun@amc.seoul.kr
Abstract
- Rhabdomyoma has been reported to be the most common type of cardiac tumors in fetuses and children, and multiple cardiac rhabdomyomas almost certainly signify the association with tuberous sclerosis. We report here on a case of Tetralogy of Fallot (ToF) that was associated with multiple rhabdomyomas and tuberous sclerosis. A two-year-old boy, who had undergone systemic-pulmonary shunt during the neonatal period, received total correction of his ToF after the complete regression of the cardiac tumor. The postoperative course was uneventful, and he has been follow-up for 2 months. The boy is currently in an excellent condition.