J Korean Neurosurg Soc.  2010 Nov;48(5):448-451. 10.3340/jkns.2010.48.5.448.

Primary Intramedullary Spinal Sarcoma : A Case Report and Review of the Current Literatures

• Kim SH
• Bak KH
• Kim DW
• Kang TH

• KMID: 1453323
• DOI: http://doi.org/10.3340/jkns.2010.48.5.448

Abstract

Primary central nervous system (CNS) sarcomas are exceedingly rare, and, to the best of our knowledge, there has not yet been a report of intramedullary sarcoma. Here, we report a primary intradural intramedullary sarcoma of the spinal cord in a four-year-old boy who presented with low back pain and a radiculopathy involving both lower extremities. The tumor showed significant enhancement on magnetic resonance (MR) images due to its extreme vascularity. Gross total tumor removal was performed with microelectrical pulse recording, and the patient also received adjuvant radiotherapy and chemotherapy. After the operation, the patient's sensory deficits were improved. Because CNS dissemination is common, entire neuraxis evaluation is essential, although there was no evidence of dissemination in this case. The prognosis of primary CNS sarcoma is poor due to infiltrative nature and early CNS dissemination is common, and the treatment of choice is radical surgical resection. Adjuvant therapy is also beneficial with radiotherapy and chemotherapy.

Keyword

Central nervous system; Intramedullary; Primary; Sarcoma

MeSH Terms

Central Nervous System
Humans
Low Back Pain
Lower Extremity
Magnetic Resonance Spectroscopy
Prognosis
Radiculopathy
Radiotherapy, Adjuvant
Sarcoma
Spinal Cord