Tuberc Respir Dis.  2011 Mar;70(3):242-246. 10.4046/trd.2011.70.3.242.

A Case of Pulmonary Capillary Hemangiomatosis-Like Lesion Followed for Seven Years

• Rhee CK
• Yim NY
• Shim S
• Kim HJ

• KMID: 1442854
• DOI: http://doi.org/10.4046/trd.2011.70.3.242

Abstract

Pulmonary capillary hemangiomatosis (PCH) is a rare disease of unknown etiology that is characterized by nodules composed of infiltrating capillary blood vessels. Herein, we describe a case of a PCH-like lesion that was detected by chest computed tomography. Transthoracic needle aspiration resulted in life-threatening hemorrhage. The patient was followed for seven years. He remained in good health and a follow up image showed little interval change.

Keyword

Hemangioma, Capillary/Diagnosis; Tomography, X-Ray Computed; Magnetic Resonance imaging

MeSH Terms

Blood Vessels
Capillaries
Follow-Up Studies
Hemorrhage
Humans
Magnetic Resonance Imaging
Needles
Rare Diseases
Thorax
Tomography, X-Ray Computed

Figure

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  Figure 1 HRCT showed ill-defined nodular densities and interlobular and intralobular septal thickenings in LUL. HRCT: high resolution computed tomography.

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  Figure 2 MRI showed reticular shaped iso-signal intensity of T1WI (A) and mottled reticular shaped high signal intensity on T2WI (B). Dysplasia of branching vessel originating from thoracic aorta was also noted on T2WI (C). MRI: magnetic resonance image; WI: weighted image.

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  Figure 3 CT-guided aspiration was performed in LUL. CT: computer tomography; LUL: left upper lobe.

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  Figure 4 Chest X-ray after TTNA showed newly developed hazy density in LUL. TTNA: transthoracic needle aspiration; LUL: left upper lobe.

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  Figure 5 CT showed ill-defined air space consolidation in LUL. CT: computer tomography; LUL: left upper lobe.

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  Figure 6 Chest X-ray showed improvement of consolidation in LUL. LUL: left upper lobe.

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  Figure 7 Chest X-ray showed further improvement of consolidation in LUL. LUL: left upper lobe.

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  Figure 8 CT showed interlobular septal thickening (A) with enhanced vascular structure (B) in LUL. CT: computer tomography; LUL: left upper lobe.

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