J Korean Pediatr Soc.
1980 Mar;23(3):252-256.
A Case of Letterer-Siwe Disease
- Affiliations
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- 1Department of Pediatrics, College of Medicaine, Ewha Womans University, Seoul, Korea.
Abstract
- The patient was presented characteristic clinical, histopathological and X-ray findings, in cluding generalized edema, petechial rash, lymphadenopathy, bone lesions, pulmonary infiltration and hepatomegaly with anemia. Most of these signs developed soon after birth. Diagnosis was confirmed by microscopic examin ation of lymph node biopsy and clinical X-ray findings. The patient was received antibiotics, corticosteroid and vinblastine and discharged against doctors order without improvement.