Yonsei Med J.  2007 Oct;48(5):865-867. 10.3349/ymj.2007.48.5.865.

A Good Outcome for a Case of Chronic Pneumonitis of Infancy

• Kim JM
• Kwon SY
• Kim ES
• Sohn MH
• Kim KE
• Kim MJ
• Cho SH

• KMID: 1122626
• DOI: http://doi.org/10.3349/ymj.2007.48.5.865

Abstract

Chronic pneumonitis of infancy (CPI) is a very rare interstitial lung disease. Its pathological features differ from other types of interstitial pneumonia that occur in adults and children. The mortality rate of CPI is high, even with treatment. We report a case of a 3 month old girl diagnosed with CPI after an open lung biopsy who improved after proper treatment.

Keyword

Infants; interstitial lung disease; chronic pneumonitis of infancy

MeSH Terms

Biopsy
Female
Humans
Infant
Lung Diseases, Interstitial/*diagnosis/drug therapy/pathology
Pneumonia/*diagnosis/drug therapy/pathology
Tomography, X-Ray Computed

Figure

• 

  Fig. 1 CT scan showing emphysematous changes in the right middle lobe. Ground glass opacities with some mosaic perfusion patterns are seen in both upper lobes (A) and lower lobes (B). Interlobular septal thickenings are also observed.

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  Fig. 2 (A) Diffuse interstitial lymphocytic infiltration and intraalveolar macrophage accumulation in lung tissue at low-magnification. (B) Diffuse interstitial lymphocytic infiltration and intraalveolar macrophage accumulation, type II pneumocyte hyperplasia observed at high magnification.

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