Korean J Ophthalmol.  2007 Jun;21(2):124-126. 10.3341/kjo.2007.21.2.124.

Bilateral Spontaneous Anterior Lens Dislocation in a Retinitis Pigmentosa Patient

• Kwon YA
• Bae SH
• Sohn YH

• KMID: 1101916
• DOI: http://doi.org/10.3341/kjo.2007.21.2.124

Abstract

PURPOSE: To report a case of bilateral spontaneous anterior lens dislocation associated with retinitis pigmentosa (RP). METHODS: A 45-year-old male with RP presented with elevated intraocular pressure (IOP) in the right eye and was treated with laser iridotomy (LI). After LI, complete crystalline lens dislocation into the anterior chamber occurred. Surgical intervention, including anterior vitrectomy, intracapsular cataract extraction (ICCE), and IOL scleral fixation was performed. Two years later, the same episode occurred in his left eye and a similar treatment was done. RESULTS: Surgery was successful in both eyes. CONCLUSIONS: This is the first report of bilateral spontaneous anterior lens dislocation in a RP patient.

Keyword

Anterior lens dislocation; Retinitis pigmentosa

MeSH Terms

*Anterior Chamber
Cataract/complications/diagnosis
Cataract Extraction
Electroretinography
Follow-Up Studies
Humans
Iris/surgery
Laser Therapy/adverse effects
Lens Implantation, Intraocular/methods
Lens Subluxation/diagnosis/*etiology/surgery
Male
Middle Aged
Ocular Hypertension/complications/physiopathology/surgery
Retinitis Pigmentosa/*complications/diagnosis/surgery
Sclera/surgery
Suture Techniques
Visual Fields
Vitrectomy

Figure

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  Fig. 1 Fundus photograph of the right (A) and left (B) eye. Bone-spicule pigmentation in the entire retina with sparing of the macula and pale optic discs were noted.

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  Fig. 2 Visual field of the right (A) and left (B) eye. Extensive peripheral field defect is noted (central 10°). Visual field using the Humphrey Visual Field Analyzer (model 750, Humphrey Instruments, Inc, Dublin, California; C24-2 program).

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  Fig. 3 (A) Scotopic ERG shows prolonged rod a-wave implicit times. (B) Oscillatory ERG. (C) Photopic ERG shows prolonged cone b-wave implicit times. (D) 30Hz Flicker ERG.

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  Fig. 4 Slit lamp photograph. (A) The preoperative photograph in the left eye with complete anterior lens dislocation. (B) The postoperative photograph in the left eye; dislocated lens was removed and posterior chamber IOL is in place.

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