Korean J Radiol.  2006 Dec;7(4):287-291. 10.3348/kjr.2006.7.4.287.

Generalized Lymphangiomatosis: Radiologic Findings in Three Pediatric Patients

• Yang DH
• Goo HW

• KMID: 1092553
• DOI: http://doi.org/10.3348/kjr.2006.7.4.287

Abstract

Generalized lymphangiomatosis is a rare disease that is characterized by widespread bony and soft tissue involvement of lymphangioma. Radiological evaluation is crucial because the site and extent of the lymphangioma are important prognostic factors. We reported here on three cases of generalized lymphangiomatosis and all three cases showed similar radiologic findings, but a different clinical course. The CT, US and MR images showed sharply defined, non-enhanced cystic lesions involving the mediastinum, bones, spleen, lung and lower neck. The whole body MR imaging with the short tau inversion recovery (STIR) sequence showed good capability for evaluating the extent of disease.

Keyword

Computed tomography (CT); Magnetic resonance (MR); Ultrasound (US); Lymphangiomatosis

MeSH Terms

Tomography, X-Ray Computed
Male
Magnetic Resonance Imaging
Lymphangioma/*diagnosis/radiography/ultrasonography
Humans
Diagnosis, Differential
Contrast Media
Child, Preschool
Child