- The Effect of Cycolooxygenase (COX-1 and COX-2) on the Bacterial Toxin Formyl Methionyl Leucyl Phenylalanine (fMLP) Induced Contraction of the Rabbit Bladder Muscle
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Jung SY, Bauer AJ
- KMID: 1914219
- Korean J Urol.
- 2000 Feb;41(2):323-327.
No abstract available. -
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- Fungal and Plant Phenylalanine Ammonia-lyase
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Hyun MW, Yun YH, Kim JY, Kim SH
- KMID: 2312651
- Mycobiology.
- 2011 Dec;39(4):257-265.
L-Phenylalanine is one of the essential amino acids that cannot be synthesized in mammals in adequate amounts to meet the requirements for protein synthesis. Fungi and plants are able to... -
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- A Case of Maternal Phenyletonuria
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Hong HK, Lee WR, Lee DW
- KMID: 2280512
- Korean J Perinatol.
- 1999 Sep;10(3):387-390.
Maternal phenylketonuria(PKU) is a disorder which appears when a pregnant woman with PKU doesn't take low phenylalanine diet, phenylalanine level of the fetus rises and interferes with fetal development and... -
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- The Effects on the MSG with Phenylalanine Treatment in the Area Postrema of the Rat Medulla
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Lee CH, Ko BM, Kim MS, Chung OB
- KMID: 2071860
- Korean J Phys Anthropol.
- 2000 Jun;13(2):213-220.
Glutamate is an amino acid neurotransmitter capable of producing widespread receptor-mediated neuronal excitation. In this experiment, we examined the effect of saline, monosodium glutamate (MSG), phenylalanine and MSG-phenylalanine treatment on... -
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- Outpatient General Anesthesia of a Patient with Phenylketonuria: A case report
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Yang SM, Seo KS, Kim HJ, Yum KW
- KMID: 2238313
- Korean J Anesthesiol.
- 2007 Jul;53(1):136-139.
- doi: 10.4097/kjae.2007.53.1.136
Phenylketonuria (PKU), an autosomal recessive disorder, occurs in one of 53,000 births in Korea. The disorder is associated with deficient activity of phenylalanine hydroxylase. In PKU, phenylalanine cannot be used... -
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- A case of two sisters births from mother with phenylketonuria lacking mental retardation
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Ki CS, Kim JK
- KMID: 2280465
- Korean J Pediatr.
- 2008 May;51(5):546-550.
- doi: 10.3345/kjp.2008.51.5.546
In this untreated classic phenylketonuria (PKU) case, mental retardation is severe; however, there have been individuals-like the mother of this case who have escaped mental retardation and all the other... -
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- Cloning and Expression Analysis of Phenylalanine Ammonia-Lyase Gene in the Mycelium and Fruit Body of the Edible Mushroom Flammulina velutipes
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Yun YH, Koo JS, Kim SH, Kong WS
- KMID: 2312830
- Mycobiology.
- 2015 Sep;43(3):327-332.
- doi: 10.5941/MYCO.2015.43.3.327
Phenylalanine ammonia-lyase (PAL) gene is known to be expressed in plants, and is involved in the differentiation, growth and synthesis of secondary metabolites. However, its expression in fungi remains to... -
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- Tissue-specific activation of mitogen-activated protein kinases for expression of transthyretin by phenylalanine and its metabolite, phenylpyruvic acid
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Park JW, Lee MH, Choi JO, Park HY, Jung SC
- KMID: 983983
- Exp Mol Med.
- 2010 Feb;42(2):105-115.
- doi: 10.3858/emm.2010.42.2.012
Phenylketonuria is an autosomal recessive disorder caused by a deficiency of phenylalanine hydroxylase. Transthyretin has been implicated as an indicator of nutritional status in phenylketonuria patients. In this study, we... -
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- Response of Achlya racemosa, A. proliferoides and Saprolegnia furcata to Sub-lethal Treatments of Amino Acids
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Ali EH
- KMID: 2312405
- Mycobiology.
- 2003 Jun;31(2):86-94.
The effect of four sub-lethal concentrations (400, 800, 1,200 and 1,600 microg/ml) of three amino acids such as isoluecine, aspartic acid and phenylalanine on vegetative growth and sexual and asexual... -
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- Two Cases of Tetrahydrobiopterin Deficiency
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Choi JW, Yang SW, Moon HR, Cho SC
- KMID: 2335149
- J Korean Pediatr Soc.
- 1995 Mar;38(3):397-403.
Tetrahydrobiopterin(BH4) deficiency is a rare type of hyperphenylalaninemia and usually leads to a progressive neurologic deterioration despite early dietary control of blood phenylalanine concentration. We experienced two cases of BH4... -
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- A Case of Tyrosinemia Type 1 with Cytomegalovirus Infection
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Cho JH, Shim KJ, Kim SK, Shin SH, Lee KH, Yun HS
- KMID: 2140987
- Korean J Pediatr.
- 2004 Jan;47(1):111-114.
Tyrosinemia type 1 is an autosomal recessive inborn error of tyrosine metabolism that caused a mutation in the gene coding for the enzyme fumarylacetoacetate hydrolase(FAH). As a result, maleylacetoacetate(MAA) and... -
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- Brain MRI Findings in PKU Patients
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Kim YH, Suh ES, Lee DW, Hong HS
- KMID: 2007351
- J Korean Child Neurol Soc.
- 2002 May;10(1):122-130.
PURPOSE: Abnormalities of magnetic resonance imaging(MRI) of the brain occur in some patients with phenylketonuria(PKU). The purpose of this study was to evaluate relation between MR findings, age and serum... -
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- Pterin & DHPR measurement and DNA analysis in Korean PKU patients
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Chong CH, Lee HY, Lee DH, Lee SJ, Cha KW, Yim JB, Okano Y
- KMID: 2208554
- J Korean Pediatr Soc.
- 1993 Dec;36(12):1681-1690.
Phenylketonuria is metabolic disorder that results from a deficiency of the hepatic phenylalanine hydroxylase. But among patients with hyperphenylalaninemia, the defect resides in one of the enzymes necessary for production... -
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- Correlation Between Gastric Emptying and Gastric Adaptive Relaxation Influenced by Amino Acids
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Uchida M, Kobayashi , Saito C
- KMID: 2387831
- J Neurogastroenterol Motil.
- 2017 Jul;23(3):400-408.
- doi: 10.5056/jnm16153
BACKGROUND/AIMS: Amino acids have many physiological activities. We report the correlation between gastric emptying and gastric adaptive relaxation using tryptophan and amino acids with a straight alkyl chain, hydroxylated chain,... -
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- Amino Acid Derangements in Plasma and Erythrocytes of Patients with Sepsis
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Chang SH, Cho KJ, Chang YJ, Song KE, Lee WK, Kim JS
- KMID: 2089495
- Korean J Clin Pathol.
- 1998 Jun;18(2):144-150.
BACKGROUND: Sepsis is a major insult leading to increased muscle breakdown and oxidation of amino acids. Disturbed plasma and brain amino acid levels may be important in the altered mental... -
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- Effects of Some Amino Acids on Ammonia Secretion and Extracellular Protease Activity by Three Oomycetes in Synthetic Medium with or without Glucose
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Ali EH
- KMID: 2052861
- Mycobiology.
- 2005 Mar;33(1):23-29.
- doi: 10.4489/MYCO.2005.33.1.023
The effects of different concentrations of three amino acids as carbon and or nitrogen sources on mycelial dry weights, changes in pH values of synthetic medium, ammonia secretion and extracellular... -
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- The Study of DNA Mutations of Phenylketonuria in Koreans
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Yoo SJ, Hong YH, Lee YW, Jung SC, Ki CS, Lee DH
- KMID: 2184444
- J Genet Med.
- 2008 Jun;5(1):26-33.
PURPOSE: Phenylketonuria(PKU) is an inborn error of metabolism and a genetic disorder resulting from a deficiency of phenylalanine hydroxylase(PAH) and decreased activity of tetrahydrobiopterin(BH4).In this study the correlation between the... -
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- Electroencephalogram in Phenylketonuria
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Kim SH, Suh ES, Lee DH
- KMID: 2024065
- J Korean Pediatr Soc.
- 1997 Jan;40(1):13-20.
PURPOSE: Abnormal electroencephalogram patterns is common findings in patients with Phenylketonuria. This study was designed to determine the importance of an abnormal EEG and the relationships among EEG findings, biochemical... -
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- Examination of lysine requirement of healthy young male adults on a Chinese habitual diet by the modified indicator amino acid oxidation method
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Tian Y, Peng J, Chen Y, Gong J, Xu H
- KMID: 2313712
- Nutr Res Pract.
- 2014 Feb;8(1):59-65.
There is currently no reference for intake of lysine for Chinese people; therefore, the present study was conducted to determine the lysine requirement of Chinese young male adults on a... -
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- Exon deletions of the phenylalanine hydroxylase gene in Italian hyperphenylalaninemics
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Cali F, Ruggeri G, Vinci M, Meli C, Carducci C, Leuzzi V, Pozzessere S, Schinocca , Ragalmuto , Chiavetta , Micciche S, Romano V
- KMID: 983980
- Exp Mol Med.
- 2010 Feb;42(2):81-86.
- doi: 10.3858/emm.2010.42.2.009
A consistent finding of many studies describing the spectrum of mutant phenylalanine hydroxylase (PAH) alleles underlying hyperphenylalaninemia is the impossibility of achieving a 100% mutation ascertainment rate using conventional gene-scanning... -
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