- Clinical study of oral branched-chain amino acids (aminoleban@ EN) in patients with hepatic encephalopathy
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Lee SI, Lee SJ, Byun KS, Lee CD, Kim BS, Chang R, Kee CS, Kwa KS, Chung JM, Moon HK, Rew JS, Yoon CM
- KMID: 1685232
- Korean J Gastroenterol.
- 1991 May;23(2):504-517.
No abstract available. -
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- A Case of Serum Amino Acid Disturbance with Hyperammonemia in Patient with Primary Amyloidosis
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Kim Y, Kim JS, Park SY, Park IH, Cheong JW, Lee ST, Min YH, Hahn JS, Kie JH
- KMID: 2252368
- Korean J Hematol.
- 2005 Mar;40(1):54-57.
- doi: 10.5045/kjh.2005.40.1.54
There have been reports that hyperammonemia and amino acid disturbance can cause loss of consciousness in patients with multiple myelomas and normal liver function. We experienced a case of a... -
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- Recent Progress on Branched-Chain Amino Acids in Obesity, Diabetes, and Beyond
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Siddik MA, Shin AC
- KMID: 2458625
- Endocrinol Metab.
- 2019 Sep;34(3):234-246.
- doi: 10.3803/EnM.2019.34.3.234
Branched-chain amino acids (BCAAs) are essential amino acids that are not synthesized in our body; thus, they need to be obtained from food. They have shown to provide many physiological... -
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- Nutrition Support in Liver Transplantation Patients
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Moon M, Yi NJ
- KMID: 1731695
- J Korean Soc Parenter Enter Nutr.
- 2013 Apr;5(1):20-23.
Malnutrition is common in cirrhotic patients undergoing liver transplantation. It has been associated with a high risk of postoperative complications and mortality rates in patients undergoing surgery. Studies have shown... -
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- A Case of Maple Syrup Urine Disease Associated with Acrodermatitis Enteropathica-like Syndrome Due to Iisoleucine Deficinecy During Diet Therapy
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Moon KH, Gwon OS, Lee JI, Rho SW, Jeon SS, Seo SS
- KMID: 2335536
- J Korean Pediatr Soc.
- 2001 Apr;44(4):469-474.
Maple syrup urine disease(MSUD) is an autosomal recessive disorder involving the metabolism of the branched-chain amino acids(BCAA) such as leucine, isoleucine and valine. The disorder is due to a defect... -
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- A Case of Maple Syrup Urine Disease
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Cho DH, Lee HM, Kim SY, Ra CS
- KMID: 1945759
- J Korean Pediatr Soc.
- 1997 Sep;40(9):1297-1302.
Maple syrup urine disease (MSUD) is an autosomal recessive disease caused by a deficiency in subunits of the branched-chain alpha-ketoacid dehydrogenase complex (BCKDH). The disease is characterized by the accumulation... -
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- Effects of Nutritional Supplementation on Nutirtional Status in Patients with Nonalcoholic Liver Cirrhosis
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Ahn SH, Kim OY, Lee JH, Kim JY, Han KH
- KMID: 2269674
- Korean J Nutr.
- 2003 Jul;36(6):577-588.
Severe protein-calorie malnutrition, common in patients with advanced liver disease, can seriously undermine the capacity for regeneration and functional restoration of liver. Nutritional supplementation for these patients can improve biochemical... -
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- Prospective Study on Efficacy of Oral Supplement of Branched-Chain Amino Acid Granules on the Nutritional Status of the Cirrhotics
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Song KH, Kim MS, Han KH, Lee KS, Chon CY, Moon YM, Ahn SH, Lee JH
- KMID: 2241231
- Korean J Hepatol.
- 2001 Dec;7(4):432-438.
BACKGROUND/AIMS: A prospective comparative study was conducted to investigate the efficacy of orally administered branched-chain amino acids (BCAA) in cirrhotic patients. METHODS: Forty-seven patients with liver cirrhosis of viral etiologies,... -
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- Effect of Oral Supplementation with Branched-chain Amino Acid (BCAA) during Radiotherapy in Patients with Hepatocellular Carcinoma: A Double-Blind Randomized Study
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Lee IJ, Seong J, Bae JI, You SH, Rhee Y, Lee JH
- KMID: 1804672
- Cancer Res Treat.
- 2011 Mar;43(1):24-31.
PURPOSE: The present study evaluated whether oral supplementation with a branched-chain amino acid (BCAA) improves the biochemical and amino acid profiles of liver tumor patients undergoing radiotherapy. MATERIALS AND METHODS: Patients... -
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- Hepatic encephalopathy
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Kim CW
- KMID: 2256159
- Korean J Med.
- 2008 Jul;75(1):27-36.
Hepatic encephalopathy, one of the major complications of cirrhosis, is a neuropsychiatric syndrome caused by accumulation of toxins in the central nervous system following dysfunction in liver detoxification. Various manifestations... -
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- A comparison of metabolomic changes in type-1 diabetic C57BL/6N mice originating from different sources
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Lee S, Kwak JH, Kim SH, Yun J, Cho JY, Kim K, Hwang D, Jung YS
- KMID: 2459300
- Lab Anim Res.
- 2018 Dec;34(4):232-238.
- doi: 10.5625/lar.2018.34.4.232
Animal models have been used to elucidate the pathophysiology of varying diseases and to provide insight into potential targets for therapeutic intervention. Although alternatives to animal testing have been proposed... -
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- Genotype and clinical features of Korean patients with methylmalonic aciduria and propionic aciduria
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Lee EH, Ko JM, Kim JM, Yoo HW
- KMID: 2280191
- Korean J Pediatr.
- 2008 Sep;51(9):964-970.
- doi: 10.3345/kjp.2008.51.9.964
PURPOSE: Methylmalonic aciduria (MMA) and propionic aciduria (PA) are inborn errors in the catabolism of branched-chain amino acids. The study was undertaken to investigate the genotypes and clinical features of... -
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- Re-Evaluation of Neonatal Screening Tests for Inborn Errors of Metabolism with Dried Filter Paper Blood Spots
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Shim KS, Hwang JS, Lim JS, Kim SY, Shin CH, Yang SW, Choi JH, Yun CK, Song JH
- KMID: 1829633
- J Korean Pediatr Soc.
- 1999 Dec;42(12):1639-1644.
PURPOSE: There have been high rates of false positive and recall in neonatal screening test using the cut-off points set by the manufacturing company. So, it is necessary to re-evaluate... -
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