Kawasaki disease is an acute febrile mucocutanenous syndrome associated with multisystemic vasculitis. The etiology of Kawasaki disease is still unknown therefore this disease can be diagnosed only based upon clinician's recognition of a symptom pattern which includes high fever, oral cavity changes, polymorphous skin rash, conjuctival injections, cervical lymphadenopathy, and swelling of peripheral extremities. Early diagnosis and treatment of Kawasaki disease is critical to reduce the risk of cardiac complications such as coronary aneurysm. However there is no specific diagnostic tools for Kawasaki disease, unusual clinical manifestation resembling infectious disease involving cervical lesion often leads to delay in appropriate diagnosis and treatment of Kawasaki disease. We report a ten-year-old girl with Kawasaki disease whose initial presentation mimicking peritonsillar abscess.