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Korean Circ J. 2009 Nov;39(11):494-498. English. Case Report. https://doi.org/10.4070/kcj.2009.39.11.494
Chung JW , Lee SJ , Lee JH , Chin JY , Lee HJ , Lee CJ , Choi YS , Shim SB , Youn HJ , Lee SH .
Division of Cardiology, Department of Internal Medicine, The Catholic University of Korea, St. Mary's Hospital, Seoul, Korea. younhj@catholic.ac.kr
Department of Internal Medicine, Daerim Saint Mary's Hospital, Seoul, Korea.
Department of Chest Surgery, The Catholic University of Korea, St. Mary's Hospital, Seoul, Korea.
Abstract

Isolated left ventricular noncompaction cardiomyopathy (IVNC) is a cardiomyopathy thought to be caused by arrest of normal embryogenesis of the endocardium and myocardium. This abnormality is often associated with other congenital cardiac defects. A 21-year-old man presented to the emergency department with worsening exertional dyspnea during the previous 2 months. Two-dimensional and Doppler echocardiography revealed an enlarged left atrium (LA) and a markedly dilated left ventricle (LV) with preserved LV systolic function, severe mitral valve regurgitation, and prolapse due to chordae rupture. The myocardium of the LV and right ventricle (RV) had excessively prominent trabeculations and deep intertrabecular recesses. He is the first patient in Korea who has undergone mitral valve replacement surgery because of severe mitral valve regurgitation and prolapse due to chordae rupture accompanied by IVNC.

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