Ectopic pancreas is defined as pancreatic tissue lacking anatomical and vascular continuity with the main body of the pancreas. Common symptoms are epigastric pain, hemorrhage, chest pain, weight loss, nausea and vomiting. A 2-month-old male patient was hospitalized because of continuous bile stained vomiting for 2 days. Abdominal ultrasonography and colon study showed malrotation of the intestine. Surgical exploration revealed the ectopic pancreas on the 10cm lower portion of Treitz ligament and rotation of terminal ileum. We performed adhesiolysis, small bowel resection and anastomosis. The diagnosis of ectopic pancreas was made by histologic examination. We report a case of ectopic pancreas with intestinal adhesion and malrotation with brief review of related literatures.