Dermoid and epidermoid of the spinal cord are rare and their percentage was 2.6% of spinal cord tumors. In dermoid average age of occurrence is 28.3 years. They are dysembryonic malformations. Dermoid consists of desquamated material, sebaceous material and hairs. The region of preference is lumbosacral spinal cords, especially cauda equina and conus medullaris. We are reporting a case of dermoid which has taken intracapsular enucleation and discuss about the epidemiology and pathogenesis.