Germ cell tumor of basal ganglia is rare. Authors report a case of mixed germ cell tumor of left basal ganglia in a 16 year-old boy who had right-sided hemiparesis and dysphasia. Brain CT scan showed highly enhancing mass lesion with cystic portion and dense tumor stain was demonstrated in carotid angiography. The patient was successfully treated by left temporal lobectomy and partial removal followed by irradiation which has resulted in good neurological status. A summary of previously reported cases is also presented.