Papilloma of the choroids plexus is rare and the incidence is about 0.4% of the verified intracranial tumors. This tumor is interesting because of its frequent association with communicating hydrocephalus and possibility of total excision with satisfactory result. We present a case of choroids plexus papilloma of the right lateral ventricle in a 5 years old girl with progressively enlarged head and walking difficulty. Pathologically the removed specimen was a 5x4x1.5 cm. sized pinkish globular mass with an irregular papillary surface. The tumor was generally edematous and showed no areas of hemorrhage or necrosis on cut sections. Microscopically the characteristic papillar consisted of single layer of mostly cuboidal and occasionally columnar epithelial cells, and were resting upon a delicate fibrous stroma containing many blood veseels. Cytoplasm of the covering epithelial cells showed slight PAS-positivity. However, neither cilia nor blepharoplast was demonstrated.