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J Korean Radiol Soc. 1987 Oct;23(5):730-735. Korean. Original Article. https://doi.org/10.3348/jkrs.1987.23.5.730
Ro HJ , Lee YI , Lee SY , Chung KS , Lee JM , Kim JW , Bahk YW .
Abstract

Hydranencephaly is a destructive or developmental disorder that results in partial or complete absence ofcerebral hemispheres with rsulting cavity, filled with CSF. But it does not involve the skull, meninnges and cerebellum. CT proved to be unique tool in diagnosis of hydranencephaly. We analysed CT findings of 6 patients with hydranencephaly who visited Catholic University Medical Colege Hospitals, during last 6 years. The resultswere as follows: 1. The male to female ratio was 1:2 and the age ranged 29 to 121 days. 2. Skull, brain stem, cerebellum and thalami were intact in all the cases. 3. Falx cerbri was fully intact in 2 cases and partiallydefective in 4 cases. 4. In 2 cases, the basal ganglia were seen bilaterally and symmetrically. 5. Remnantcerebral hemispheres were as follows; Partial and bilateral occipital lobes in all the cases. Partial andunilateral frontoparietal lobe in 1 case. Partial and bilateral temporal lobes in 1 case. 6. All resultingcavities were filled with fluid. 7. In all the cases, 3rd and 4th ventricles were present. Among the cases, 3cases showed choroid plexus and lateral ventricles, communicating with cavity bilaterally. 8. One case showed bilateral thickening of meningeal structures which was separated from the inner table of the skull.

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