Spinal muscular atrophy (SMA) is a rare lower motor neuron disease in which anesthetic management is often difficult, because the patients usually have muscle weakness and hypersensitivity to muscle relaxants. We describe the anesthesia for a 8 year-old girl with type II SMA who presented for a lower lid epiblepharon repair. We chose to use intravenous anesthesia based on propofol and remifentanil without any muscle relaxants. The peri-operative course was completely uneventful. We consider that intravenous anesthesia without muscle relaxants could be a good anesthetic choice for a patient with SMA undering general anesthesia.