Journal Browser Advanced Search Help
Journal Browser Advanced search HELP
-
J Korean Soc Plast Reconstr Surg. 2009 Jul;36(4):481-484. Korean. Case Report.
Moh JS , Na YC .
Department of Plastic & Reconstructive Surgery, Wonkwang University School of Medicine, Iksan, Jeollabuk-do, Korea. ycnadr@hanmail.net
Abstract

PURPOSE: Cleidocranial dysostosis is a rare hereditary disorder affecting bones that develop by intramembranous formation. The typical features include excessive growth of transverse diameter of the skull, hypoplastic clavicles, low height and characteristic facial features. METHODS: A 28-year-old female patient visited by frontal area depression. The diagnosis was performed by computed tomographic study and radiographic imaging. The patient had widely opened anterior fontanelle, partial fused metopic suture, multiple wormian bone and supernumenary impacted teeth. Under the coronal incision, we exposed depressed frontal area and corrected with Medpor block carving. RESULTS: Postoperatively frontoparietal skull was aestheticlly improved and satisfied the patient. CONCLUSION: Authors report a case of cleiodocranial dysostosis who underwent correction of abnormal skull shape by Medpor(R) insertion.

Copyright © 2019. Korean Association of Medical Journal Editors.