This is a case report of juvenile xanthogranulomas which developed at cutaneous lesions are rare and characterized by asymptomatic multiple cutaneous lesions and extracutaneous lesions. Juvenile xanthogranulomas are benign, usually asymptomatic, self healing yellowish papules and nodules composed of histiocytic cells that predominantly occur in infancy and childhood. Papules or nodules occur in the skin, eyes, and viscera. Juvenile xanthogranuloma is characterized histologically by a dense, sheetlike, well-demarcated histiocytic infiltration within the papillary and reticular dermis, with occasional extension into subcutaneous tissue, fascia, and peripheral muscle. We report a case of juvenile xanthogranuloma developed in a 3-months- old male infant which showed mulitiple cutaneous lesions and viscera involved the lung, heart, liver, pancreas, and testicle.