J Korean Med Sci.
1998 Oct;13(5):548-550. 10.3346/jkms.1998.13.5.548.
Acute hemolytic crisis with fulminant hepatic failure as the first manifestation of Wilson's disease: a case report
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- 1Department of Internal Medicine, Chonnam National University Medical School, Kwangju, Korea.
- KMID: 645218
- DOI: http://doi.org/10.3346/jkms.1998.13.5.548
Abstract
- We report a 27-year-old woman who developed Coombs' negative hemolytic anemia and fulminant hepatic failure as the initial manifestation of Wilson's disease. Unmeasurably low level of serum alkaline phosphatase provided a clue to the diagnosis of Wilson's disease. The diagnosis was established with the presence of Kayser-Fleischer ring, decreased serum ceruloplasmin level, and elevated urine and serum copper levels. In spite of repeated plasmapheresis, she died of multiorgan failure on the fifth hospital day.
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