Korean J Otorhinolaryngol-Head Neck Surg.  2023 Dec;66(12):878-882. 10.3342/kjorl-hns.2023.00850.

A Case of Three Ectodermal Origin Congenital Anomalies Including Congenital Mastoid Cholesteatoma

• Seo W
• Baek M
• Bahn, J
• Chung JH

• KMID: 2549471
• DOI: http://doi.org/10.3342/kjorl-hns.2023.00850

Abstract

There are several congenital anomalies of the mastoid and external ear. The external ear and mastoid form during the developmental process through the differentiation of ectoderm and mesoderm, and anomalies can arise at various stages. While most congenital anomalies can be easily diagnosed through physical examination, some cases, such as congenital mastoid cholesteatoma, may delay diagnoses. We present a successfully treated case that involved the removal of three simultaneous congenital anomalies of ectodermal origin, which included preauricular fistula, congenital mastoid cholesteatoma, and postauricular epidermal cyst, all found on one ear in a single patient.

Keyword

Congenital cholesteatoma; Epidermal cyst; Preauricular fistulae