J Korean Assoc Oral Maxillofac Surg.  2023 Aug;49(4):223-227. 10.5125/jkaoms.2023.49.4.223.

Midline cleft of the upper lip associated with a microform unilateral cleft and a proboscis-like structure: a case report

  • 1Department of Surgery, Benjamin Carson Snr School of Medicine, Babcock University, Ilishan-Remo, Nigeria
  • 2Dental Unit, Babcock University Teaching Hospital, Ilishan-Remo, Nigeria
  • 3Department of Oral and Maxillofacial Surgery, Obafemi Awolowo University, Ile-Ife, Nigeria
  • 4Department of Biochemistry, Babcock University, Ilishan-Remo, Nigeria


A midline or median cleft lip is rare, and a midline cleft associated with a unilateral cleft and a proboscis-like structure is rarer still. We present a case managed at our center in which a 5-year-old male had a median cleft of the upper lip with an associated ‘proboscis’ and a microform unilateral cleft lip.


Midline cleft; Atypical cleft; Cutaneous mass


  • Fig. 1 Preoperative clinical photographs showing the midline and microform cleft lip, bifid columella, and bifid frenula.

  • Fig. 2 A, B. Computerized tomography (CT) showing the nasal septum and falx cerebri in the patient with a true median cleft of the upper lip. These structures are absent in false median clefts.

  • Fig. 3 Schematic diagram showing the patient’s face and intraoperative procedures.

  • Fig. 4 Postoperative clinical photographs. A. Two-week follow-up. B. 24-week follow-up.



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