Adv Pediatr Surg.  2022 Jun;28(1):26-30. 10.13029/aps.2022.28.1.26.

A 13-Year Boy With Peripheral Vascular Disease and Internal Jugular Vein Thrombosis: Rare Presentation of Pheochromocytoma-Paraganglioma, “The Great Masquerader”

• Agrawal N
• Singh R
• Yadav N
• Yadav SK
• Silodia A

• KMID: 2538286
• DOI: http://doi.org/10.13029/aps.2022.28.1.26

Abstract

Catecholamine-producing tumors are rare, and the classical symptoms include maintained or paroxysmal hypertension, headaches, palpitations and sweating. However, its symptoms can vary greatly, which is why it has been called “the great masquerader.” We are reporting case of a patient with a left adrenal pheochromocytoma with multiple abdominal paragangliomas who presented with severe ischemic involvement of both the upper and lower limbs due to catecholamine induced vasospasm.

Keyword

Pheochromocytoma; Paraganglioma; Peripheral vascular diseases; Venous thrombosis