Tuberc Respir Dis.  1978 Jun;25(2):93-98. 10.4046/trd.1978.25.2.93.

A case of Isolated Congenital Absence of the Right Pulmonary Artery

• KMID: 2528926
• DOI: http://doi.org/10.4046/trd.1978.25.2.93

Abstract

In 1868, Franzel reported a case of absence of the right Pulmonary artery, associated with multiple congenital cardiac anomalies as an incidental autopsy findings, and in 1952 Madoff and associates reported the first clinically diagnozed case, of a 14-year-old female and this case was confirmed by angiocardiography. In 1956, Emmanuel and Pattison were to count a total of 46 such cases, most of which had been added because of newly refined angiocardiographic techniques. Previous reviews showed that, in gederal, absence of the right pulmonary artery appeared as an isolaled defect, but absence of the left pulmonary artery was associated with several major abnormalities of the heart and great vessels. A case of isolated congenital absence of the right pulmonary artery, diagnozed clinicaIly by angiocardiography, is presented with review. Possible embryogenesis, radiographic and angiocardiographic appearance of this condition is reviewed.