Cardiovasc Imaging Asia.  2021 Oct;5(4):162-164. 10.22468/cvia.2021.00248.

CT in Demonstrating an Extremely Rare Left-Sided Partial Morphologically Right Pulmonary Artery Sling

• Amal MY
• Chen SJ

• KMID: 2522193
• DOI: http://doi.org/10.22468/cvia.2021.00248

Abstract

A partial pulmonary artery sling in bronchopulmonary situs inversus with association of congenital distal trachea stenosis is an extremely rare vascular developmental anomaly. Understanding of this unusual anomaly requires deep knowledge of pulmonary arterial embryogenesis. We present an asymptomatic pediatric female after a one-stage operation for TaussigBing anomaly and coarctation of the aorta. Contrast-enhanced cardiac CT examination clearly demonstrated partial sling of the pulmonary artery from the right hemithorax and running a course behind the carina and in front of the esophagus before heading to the left hemithorax. Congenital distal trachea stenosis should specifically be evaluated due to strong association with complete cartilaginous rings in majority cases.

Keyword

Pulmonary artery; Multidetector computed tomography; Tracheal stenosis