Cardiovasc Imaging Asia.  2021 Oct;5(4):160-161. 10.22468/cvia.2021.00199.

A Case of Double Orifice Mitral Valve in a Patient with Bicuspid Aortic Valve: Coincidental or a Missed Finding?

• Buttar R
• Khosa GS
• Baibhav B

• KMID: 2522192
• DOI: http://doi.org/10.22468/cvia.2021.00199

Abstract

A 63-year-old male with past medical history of bicuspid aortic valve and ascending aortic aneurysm was referred to cardiology for aortic valve replacement (AVR) and aneurysm repair. Transthoracic echocardiogram (TTE) showed bicuspid aortic valve with severe aortic valve stenosis. Patient underwent transesophageal echocardiogram which showed an incidental finding of double orifice mitral valve (DOMV) with fusion of A/P cusps along anterolateral commissure not noted on previous TTE. Patient underwent AVR with bioprosthetic aortic valve along with resection and replacement of the ascending aortic aneurysm. No intervention was performed for the asymptomatic DOMV. DOMV is a rare congenital cardiac abnormality, easily missed on routine TTE. It warrants need for careful evaluation of mitral valve apparatus in patients with other congenital cardiac abnormalities known to be associated with DOMV.

Keyword

Mitral valve; Bicuspid aortic valve disease; Three-dimensional echocardiography; Transesophageal echocardiography; Heart valve disease