Korean J Med.  2021 Oct;96(5):438-442. 10.3904/kjm.2021.96.5.438.

A Rare Case of Fibromuscular Dysplasia with Postpartum Renal Artery Rupture in a Non-Hypertensive Woman

• Kim EE
• Won Y
• Kim YH
• Shin I
• Kim YO

• KMID: 2522018
• DOI: http://doi.org/10.3904/kjm.2021.96.5.438

Abstract

Fibromuscular dysplasia (FMD) of the renal artery is a non-atherosclerotic, non-inflammatory vascular disease that causes stenosis, aneurysm, dissection, and occlusion of the vessel. We report a rare case of a postpartum FMD patient who presented with spontaneous acute perirenal hematoma due to renal artery aneurysm rupture after cesarean section. The 40-year-old patient presented with sudden onset of abdominal pain 2 days after an elective cesarean section performed at full gestational term. A computed tomography scan of the abdomen revealed perirenal hematomas with signs of FMD in both renal arteries. The bleeding was successfully controlled by transcatheter arterial embolization. Short-term continuous renal replacement therapy was performed until her renal function recovered. FMD of the renal artery is rare in pregnant patients. Additionally, aneurysm rupture can be life threatening and requires immediate medical attention and prompt management.

Keyword

섬유근육형성이상; 신동맥류; 색전술; Fibromuscular dysplasia; Postpartum hemorrhage; Renal artery