Korean J Otorhinolaryngol-Head Neck Surg.  2021 Aug;64(8):599-603. 10.3342/kjorl-hns.2020.01088.

A Case of the Hamartoma of Middle Ear Presenting with the Aplasia of Ipsilateral Internal Carotid Artery

• Kim S
• Pak MG
• Jeong SW

• KMID: 2519760
• DOI: http://doi.org/10.3342/kjorl-hns.2020.01088

Abstract

Hamartoma is a benign congenital tumor made of an abnormal mixture of normal tissues. It is a kind of developmental anomaly, in which the tissues are arranged with an excess growth of one or more of its components. Hamartoma is usually found in the lung, hypothalamus, and colon, but very rarely found in the head and neck areas. Symptoms are caused by the tumor tissue pressing against other tissues or organs. Surgical removal is the treatment modality of choice for hamartomas causing symptoms. The aplasia of unilateral internal carotid artery (ICA) is a rare congenital anomaly. ICA aplasia can cause structural change of the middle ear space. A 5 year-old female patient was presented with large hamartoma in the middle ear and the aplasia of the ipsilateral ICA. The mass was successfully removed without any complications. Authors report this case with a brief literature review.

Keyword

Hamartoma; Internal carotid artery diseases; Middle ear